3-Methyl-2-oxobutanoic acid

3-Methyl-2-oxobutanoic acid

AT5232

CAS 759-05-7

More details

1000 Items

$48.00

$48.00 per 100 mg

Overview

3-Methyl-2-oxobutanoic acid (2-Oxoisovaleric acid) is an abnormal metabolite that arises from the incomplete breakdown of branched-chain amino acids. 3-Methyl-2-oxobutanoic acid is a neurotoxin, an acidogen, and a metabotoxin. A neurotoxin causes damage to nerve cells and nerve tissues. 3-Methyl-2-oxobutanoic acid is a keto-acid, which is a subclass of organic acids. Abnormally high levels of organic acids in the blood (organic acidemia), urine (organic aciduria), the brain, and other tissues lead to general metabolic acidosis.

Chemical Properties

Molecular FormulaC5H8O3
Molecular Weight116.12
CAS Numbers759-05-7
SolubilityDMSO
Purity98% by HPLC
SMILES CodeCC(C)C(=O)C(O)=O

Storage and Handling

0C Short Term, -20C Long Term

References

Yudkoff M, et al. Brain amino acid requirements and toxicity the example of leucine. J Nutr. 2005 Jun;135[6 Suppl] 1531S-8S.